ARHGAP31

Rho GTPase activating protein 31

Normal Function

Health Conditions Related to Genetic Changes

Adams-Oliver syndrome

At least three mutations in the ARHGAP31 gene are known to cause Adams-Oliver syndrome, a condition characterized by areas of missing skin (aplasia cutis congenita), usually on the scalp, and malformations of the hands and feet. These mutations lead to production of an abnormally short ARHGAP31 protein that is more active than normal. The increased GAP activity leads to a reduction in Cdc42 and Rac1 signaling, which impairs proper development of the skin on the top of the head and the bones in the hands and feet.

More About This Health Condition

Related Conditions

Adams-Oliver syndrome

Health Conditions Related to Genetic Changes

At least three mutations in the ARHGAP31 gene are known to cause Adams-Oliver syndrome, a condition characterized by areas of missing skin (aplasia cutis congenita), usually on the scalp, and malformations of the hands and feet. These mutations lead to production of an abnormally short ARHGAP31 protein that is more active than normal. The increased GAP activity leads to a reduction in Cdc42 and Rac1 signaling, which impairs proper development of the skin on the top of the head and the bones in the hands and feet.