ELOVL4

ELOVL fatty acid elongase 4

Normal Function

Health Conditions Related to Genetic Changes

Stargardt macular degeneration

A few variants (also called mutations) in the ELOVL4 gene have been found to cause Stargardt macular degeneration. These variants create a premature stop signal in the instructions used to make the ELOVL4 protein. This causes the protein to form clumps (aggregates) in the endoplasmic reticulum of photoreceptors. These aggregates cannot make very long-chain fatty acids and may interfere with cell functions, ultimately leading to cell death. The loss of photoreceptors causes progressive vision loss in people with Stargardt macular degeneration.

More About This Health Condition

Related Conditions

Stargardt macular degenerationAge-related macular degeneration

Health Conditions Related to Genetic Changes

A few variants (also called mutations) in the ELOVL4 gene have been found to cause Stargardt macular degeneration. These variants create a premature stop signal in the instructions used to make the ELOVL4 protein. This causes the protein to form clumps (aggregates) in the endoplasmic reticulum of photoreceptors. These aggregates cannot make very long-chain fatty acids and may interfere with cell functions, ultimately leading to cell death. The loss of photoreceptors causes progressive vision loss in people with Stargardt macular degeneration.

MedlinePlus Genetics provides information about Age-related macular degeneration