MAP2K2

mitogen-activated protein kinase kinase 2

Normal Function

Health Conditions Related to Genetic Changes

Cardiofaciocutaneous syndrome

At least 13 mutations in the MAP2K2 gene have been identified in people with cardiofaciocutaneous syndrome. Most of these mutations change single protein building blocks (amino acids) in MEK2 protein kinase, although one mutation deletes several amino acids from the protein. These genetic changes abnormally activate MEK2 kinase, which disrupts the tightly regulated RAS/MAPK signaling pathway in cells throughout the body. The altered signaling interferes with the normal development of many organs and tissues, resulting in the characteristic features of cardiofaciocutaneous syndrome.

More About This Health Condition

Related Conditions

Cardiofaciocutaneous syndrome

Health Conditions Related to Genetic Changes

At least 13 mutations in the MAP2K2 gene have been identified in people with cardiofaciocutaneous syndrome. Most of these mutations change single protein building blocks (amino acids) in MEK2 protein kinase, although one mutation deletes several amino acids from the protein. These genetic changes abnormally activate MEK2 kinase, which disrupts the tightly regulated RAS/MAPK signaling pathway in cells throughout the body. The altered signaling interferes with the normal development of many organs and tissues, resulting in the characteristic features of cardiofaciocutaneous syndrome.